Q89.81 - Kabuki syndrome

  • Applicable to Kabuki syndrome
  • The 2026 edition of ICD10-CM Q89.81 became effective on October 1, 2025.
  • This is the American ICD10-CM version of Q89.81 - other international versions of ICD10 Q89.81 may differ.
  • Q89.81 is a Billable / Specific ICD10-CM code that can be used to indicate a diagnosis for reimbursement purposes.

 Inclusion Term

  • Kabuki syndrome, type 1, due to KMT2D mutation
  • Kabuki syndrome, type 2, due to KDM6A mutation
  • Niikawa-Kuroki syndrome

The following codes above Q89.81 contain annotation back-references that may be applicable to Q89.81:

Chapter: Q00-QA0 Congenital malformations, deformations, chromosomal abnormalities, and genetic disorders

Section: Q80-Q89 Other congenital malformations

Category: Q89 Other congenital malformations, not elsewhere classified

kabuki icd 10
 
syndrome icd 10
 
Billable/Specific Code

Browse other similar CM codes

Q89.0
 
Q89.01
 
Q89.09
 
Q89.1
 
Q89.2
 
Q89.3
 
Q89.4
 
Q89.7
 
Q89.8
 
Q89.81
 
Q89.89
 
Q89.9
 

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