E88.43 - Disorders of mitochondrial tRNA synthetases

  • Applicable to Disorders of mitochondrial tRNA synthetases
  • The 2026 edition of ICD10-CM E88.43 became effective on October 1, 2025.
  • This is the American ICD10-CM version of E88.43 - other international versions of ICD10 E88.43 may differ.
  • E88.43 is a Billable / Specific ICD10-CM code that can be used to indicate a diagnosis for reimbursement purposes.

 Inclusion Term

  • ARS2-related mitochondrial disorders
  • LBSL
  • Leukoencephalopathy with brainstem - spinal cord involvement - lactate elevation
  • Leukoencephalopathy with thalamus - brainstem involvement - high lactate
  • LTBL
  • Mitochondrial aminoacyl-tRNA synthetase disorders

codeAlso

  • , if applicable, associated condition such as:
  • leukoencephalopathy (G93.49)

The following codes above E88.43 contain annotation back-references that may be applicable to E88.43:

Chapter: E00-E89 Endocrine, nutritional and metabolic diseases

Section: E70-E88 Metabolic disorders

Category: E88 Other and unspecified metabolic disorders

synthetases icd 10
 
mitochondrial icd 10
 
disorders icd 10
 
Billable/Specific Code

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