Billable/Specific ICD-10-CM Codes - Page 37

There are 35,750 ICD-10-CM codes which are billable/specific and can be used to indicate a diagnosis for reimbursement purposes as there are no codes with a greater level of specificity under each code.

  • E72.59 - Other disorders of glycine metabolism
  • E72.81 - Disorders of gamma aminobutyric acid metabolism
  • E72.89 - Other specified disorders of amino-acid metabolism
  • E72.9 - Disorder of amino-acid metabolism, unspecified
  • E73.0 - Congenital lactase deficiency
  • E73.1 - Secondary lactase deficiency
  • E73.8 - Other lactose intolerance
  • E73.9 - Lactose intolerance, unspecified
  • E74.00 - Glycogen storage disease, unspecified
  • E74.01 - von Gierke disease
  • E74.02 - Pompe disease
  • E74.03 - Cori disease
  • E74.04 - McArdle disease
  • E74.05 - Lysosome-associated membrane protein 2 [LAMP2] deficiency
  • E74.09 - Other glycogen storage disease
  • E74.10 - Disorder of fructose metabolism, unspecified
  • E74.11 - Essential fructosuria
  • E74.12 - Hereditary fructose intolerance
  • E74.19 - Other disorders of fructose metabolism
  • E74.20 - Disorders of galactose metabolism, unspecified
  • E74.21 - Galactosemia
  • E74.29 - Other disorders of galactose metabolism
  • E74.31 - Sucrase-isomaltase deficiency
  • E74.39 - Other disorders of intestinal carbohydrate absorption
  • E74.4 - Disorders of pyruvate metabolism and gluconeogenesis
  • E74.810 - Glucose transporter protein type 1 deficiency
  • E74.818 - Other disorders of glucose transport
  • E74.819 - Disorders of glucose transport, unspecified
  • E74.820 - SLC13A5 Citrate Transporter Disorder
  • E74.829 - Other disorders of citrate metabolism
  • E74.89 - Other specified disorders of carbohydrate metabolism
  • E74.9 - Disorder of carbohydrate metabolism, unspecified
  • E75.00 - GM2 gangliosidosis, unspecified
  • E75.01 - Sandhoff disease
  • E75.02 - Tay-Sachs disease
  • E75.09 - Other GM2 gangliosidosis
  • E75.10 - Unspecified gangliosidosis
  • E75.11 - Mucolipidosis IV
  • E75.19 - Other gangliosidosis
  • E75.21 - Fabry (-Anderson) disease
  • E75.22 - Gaucher disease
  • E75.23 - Krabbe disease
  • E75.240 - Niemann-Pick disease type A
  • E75.241 - Niemann-Pick disease type B
  • E75.242 - Niemann-Pick disease type C
  • E75.243 - Niemann-Pick disease type D
  • E75.244 - Niemann-Pick disease type A/B
  • E75.248 - Other Niemann-Pick disease
  • E75.249 - Niemann-Pick disease, unspecified
  • E75.25 - Metachromatic leukodystrophy
  • E75.26 - Sulfatase deficiency
  • E75.27 - Pelizaeus-Merzbacher disease
  • E75.28 - Canavan disease
  • E75.29 - Other sphingolipidosis
  • E75.3 - Sphingolipidosis, unspecified
  • E75.4 - Neuronal ceroid lipofuscinosis
  • E75.5 - Other lipid storage disorders
  • E75.6 - Lipid storage disorder, unspecified
  • E76.01 - Hurler's syndrome
  • E76.02 - Hurler-Scheie syndrome
  • E76.03 - Scheie's syndrome
  • E76.1 - Mucopolysaccharidosis, type II
  • E76.210 - Morquio A mucopolysaccharidoses
  • E76.211 - Morquio B mucopolysaccharidoses
  • E76.219 - Morquio mucopolysaccharidoses, unspecified
  • E76.22 - Sanfilippo mucopolysaccharidoses
  • E76.29 - Other mucopolysaccharidoses
  • E76.3 - Mucopolysaccharidosis, unspecified
  • E76.8 - Other disorders of glucosaminoglycan metabolism
  • E76.9 - Glucosaminoglycan metabolism disorder, unspecified
  • E77.0 - Defects in post-translational modification of lysosomal enzymes
  • E77.1 - Defects in glycoprotein degradation
  • E77.8 - Other disorders of glycoprotein metabolism
  • E77.9 - Disorder of glycoprotein metabolism, unspecified
  • E78.00 - Pure hypercholesterolemia, unspecified
  • E78.01 - Familial hypercholesterolemia
  • E78.1 - Pure hyperglyceridemia
  • E78.2 - Mixed hyperlipidemia
  • E78.3 - Hyperchylomicronemia
  • E78.41 - Elevated Lipoprotein(a)
  • E78.49 - Other hyperlipidemia
  • E78.5 - Hyperlipidemia, unspecified
  • E78.6 - Lipoprotein deficiency
  • E78.70 - Disorder of bile acid and cholesterol metabolism, unspecified
  • E78.71 - Barth syndrome
  • E78.72 - Smith-Lemli-Opitz syndrome
  • E78.79 - Other disorders of bile acid and cholesterol metabolism
  • E78.81 - Lipoid dermatoarthritis
  • E78.89 - Other lipoprotein metabolism disorders
  • E78.9 - Disorder of lipoprotein metabolism, unspecified
  • E79.0 - Hyperuricemia without signs of inflammatory arthritis and tophaceous disease
  • E79.1 - Lesch-Nyhan syndrome
  • E79.2 - Myoadenylate deaminase deficiency
  • E79.81 - Aicardi-Goutières syndrome
  • E79.82 - Hereditary xanthinuria
  • E79.89 - Other specified disorders of purine and pyrimidine metabolism
  • E79.9 - Disorder of purine and pyrimidine metabolism, unspecified
  • E80.0 - Hereditary erythropoietic porphyria
  • E80.1 - Porphyria cutanea tarda
  • E80.20 - Unspecified porphyria